Successful surgical correction of right&sided congenital diaphragmatic hernia with critical pulmonary hypoplasia

Authors

  • O.K Sliеpov Center of Neonatal Surgery of Congenital Malformations and its Rehabilitation SI «Institute of Pediatrics, Obstetrics and Gynecology named after academician O.M. Lukyanova NAMS of Ukraine», Ukraine
  • O.P. Ponomarenko Center of Neonatal Surgery of Congenital Malformations and its Rehabilitation SI «Institute of Pediatrics, Obstetrics and Gynecology named after academician O.M. Lukyanova NAMS of Ukraine», Ukraine
  • M.Y. Migur Center of Neonatal Surgery of Congenital Malformations and its Rehabilitation SI «Institute of Pediatrics, Obstetrics and Gynecology named after academician O.M. Lukyanova NAMS of Ukraine», Ukraine
  • L.F. Sliеpova Center of Neonatal Surgery of Congenital Malformations and its Rehabilitation SI «Institute of Pediatrics, Obstetrics and Gynecology named after academician O.M. Lukyanova NAMS of Ukraine», Ukraine
  • O.P. Gladyshko Center of Neonatal Surgery of Congenital Malformations and its Rehabilitation SI «Institute of Pediatrics, Obstetrics and Gynecology named after academician O.M. Lukyanova NAMS of Ukraine», Ukraine
  • O.M. Dorosheva Center of Neonatal Surgery of Congenital Malformations and its Rehabilitation SI «Institute of Pediatrics, Obstetrics and Gynecology named after academician O.M. Lukyanova NAMS of Ukraine», Ukraine
  • G.V. Golopapa Center of Neonatal Surgery of Congenital Malformations and its Rehabilitation SI «Institute of Pediatrics, Obstetrics and Gynecology named after academician O.M. Lukyanova NAMS of Ukraine», Ukraine

DOI:

https://doi.org/10.15574/PP.2020.82.102

Keywords:

congenital diaphragmatic hernia, right-sided, herniation of the liver, critical hypoplasia of the lungs, surgical correction, newborn baby

Abstract

Congenital diaphragmatic hernia (CDH) in newborns remains a highly lethal malformation worldwide. It is characterized by migration of organs from the abdominal to the chest cavity due to a diaphragmatic defect. The major factors affecting the survival of these children are: the degree of lungs and heart hypoplasia, the presence of concomitant pathology, and the side of the diaphragm defect. In recent years, there has been an increase in survival in newborns with CDH. However, these data can vary significantly across countries, as well as approaches to diagnosing and treating this severe malformation. The survival of newborns with right-sided CDH, liver hernia, and a critical volume of lung hypoplasia is still a problem.

A clinical case of successful surgical treatment of a newborn child with a congenital malformation — a right-sided diaphragmatic hernia, with herniation of the liver, gall bladder and small intestine, critical hypoplasia of the lungs detected prenatally (ultrasound, MRI) is presented. Preoperative stabilization and surgical treatment were carried out: laparotomy, reduction of hernial contents and plastic of the diaphragm defect with local tissues. The result of surgical correction of the presented malformation is recovery.

 

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Published

2020-06-29

Issue

No. 2(78) (2020): Ukrainian Journal of Perinatology and Pediatrics

Section

Clinical case

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